Neonatal haemochromatosis with reversible pituitary involvement.

نویسندگان

  • Giuseppe Indolfi
  • Rita Bèrczes
  • Isabella Pelliccioli
  • Michela Bosisio
  • Cristina Agostinis
  • Massimo Resti
  • Marco Zambelli
  • Alessandro Lucianetti
  • Michele Colledan
  • Lorenzo D'Antiga
چکیده

Neonatal haemochromatosis is a rare alloimmune gestational disease with a high mortality. The hallmark of neonatal haemochromatosis is severe neonatal liver failure associated with extrahepatic siderosis. Thus far, no pituitary dysfunction has been reported to result from the tissue damage associated with extrahepatic siderosis. The present report describes a neonate with neonatal haemochromatosis and secondary hypothyroidism associated with pituitary iron deposition. Both the conditions were successfully treated by ABO-incompatible liver transplantation. Pituitary gland dysfunction is another possible extrahepatic manifestation of neonatal haemochromatosis, and it is reversible after liver transplantation.

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عنوان ژورنال:
  • Transplant international : official journal of the European Society for Organ Transplantation

دوره 27 8  شماره 

صفحات  -

تاریخ انتشار 2014